Clinical feature: 

Definition: Congenital hyperinsulinism, nesidioblastosis is the most common cause of persistent hypoglycemia in infancy which is caused by increased insulin secretion despite of low blood glycose levels. The most important complication is cerebral damage as a result of prolonged hypoglycemia. Type 4 of the disease is caused by HADH mutations.

Literature: 

Clayton PT et al. (2001) Hyperinsulinism in short-chain L-3-hydroxyacyl-CoA dehydrogenase deficiency reveals the importance of beta-oxidation in insulin secretion.
Gotlin RW et al. (1970) Neonatal hypoglycaemia, hyperinsulinism, and absence of pancreatic alpha-cells.
Molven A et al. (2004) Familial hyperinsulinemic hypoglycemia caused by a defect in the SCHAD enzyme of mitochondrial fatty acid oxidation.
Molven A et al. (2002) Hunting for a hypoglycemia gene: severe neonatal hypoglycemia in a consanguineous family.
Vidnes J et al. (1977) Glucagon deficiency causing severe neonatal hypoglycemia in a patient with normal insulin secretion.